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Journal article

Long term outcomes of 176 patients with X-linked hyper IgM syndrome treated with or without hematopoietic cell transplantation

Abstract:

BACKGROUND: X-linked hyper IgM syndrome (XHIGM) is a primary immunodeficiency with high morbidity and mortality compared to normal individuals. Hematopoietic cell transplant (HCT) has been considered a curative therapy, but the procedure has inherent complications, and may not be available for all patients.
OBJECTIVES: We sought to collect data on the clinical presentation, treatment, and follow-up of a large sample of patients with XHIGM in order to (1) compare long-term overall...

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Publication status:
Published
Peer review status:
Peer reviewed
Version:
Accepted manuscript

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Publisher copy:
10.1016/j.jaci.2016.07.039

Authors


de la Morena, MT More by this author
Leonard, D More by this author
Torgerson, TR More by this author
Cabral-Marques, O More by this author
Slatter, M More by this author
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Jeffrey Modell Foundation More from this funder
Publisher:
Elsevier Publisher's website
Journal:
Journal of Allergy and Clinical Immunology Journal website
Volume:
139
Issue:
4
Pages:
1282-1292
Publication date:
2016-09-30
Acceptance date:
2016-07-26
DOI:
EISSN:
1097-6825
ISSN:
0091-6749
Pubs id:
pubs:653013
URN:
uri:d6d75a9e-d449-4450-a6c7-97227d89d44a
UUID:
uuid:d6d75a9e-d449-4450-a6c7-97227d89d44a
Local pid:
pubs:653013

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