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Perturbing LSD1 and WNT rewires transcription to synergistically induce AML differentiation

Abstract:

Impaired differentiation is a hallmark of myeloid malignancies1,2. Therapies that enable cells to circumvent the differentiation block, such as all-trans retinoic acid (ATRA) and arsenic trioxide (ATO), are by and large curative in acute promyelocytic leukaemia3, but whether ‘differentiation therapy’ is a generalizable therapeutic approach for acute myeloid leukaemia (AML) and beyond remains incompletely understood. Here we demonstrate that simultaneous inhibition of the histone demethylase LSD1 (LSD1i) and the WNT pathway antagonist GSK3 kinase4 (GSK3i) robustly promotes therapeutic differentiation of established AML cell lines and primary human AML cells, as well as reducing tumour burden and significantly extending survival in a patient-derived xenograft mouse model. Mechanistically, this combination promotes differentiation by activating genes in the type I interferon pathway via inducing expression of transcription factors such as IRF7 (LSD1i) and the co-activator β-catenin (GSK3i), and their selective co-occupancy at targets such as STAT1, which is necessary for combination-induced differentiation. Combination treatment also suppresses the canonical, pro-oncogenic WNT pathway and cell cycle genes. Analysis of datasets from patients with AML suggests a correlation between the combination-induced transcription signature and better prognosis, highlighting clinical potential of this strategy. Collectively, this combination strategy rewires transcriptional programs to suppress stemness and to promote differentiation, which may have important therapeutic implications for AML and WNT-driven cancers beyond AML.

Publication status:
Published
Peer review status:
Peer reviewed

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Publisher copy:
10.1038/s41586-025-08915-1

Authors

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Institution:
University of Oxford
Division:
MSD
Department:
NDM
Sub department:
Oxford Ludwig Institute
Role:
Author
ORCID:
0000-0001-8229-832X
More by this author
Role:
Author
ORCID:
0000-0003-4022-4394
More by this author
Institution:
University of Oxford
Division:
MSD
Department:
NDM
Sub department:
Oxford Ludwig Institute
Role:
Author
ORCID:
0000-0001-6457-6365
More by this author
Institution:
University of Oxford
Division:
MSD
Department:
NDM
Sub department:
Oxford Ludwig Institute
Role:
Author
ORCID:
0000-0002-6508-1337


More from this funder
Funder identifier:
https://ror.org/03h2bh287


Publisher:
Springer Nature
Journal:
Nature More from this journal
Volume:
642
Issue:
8067
Pages:
508-518
Publication date:
2025-04-16
Acceptance date:
2025-03-18
DOI:
EISSN:
1476-4687
ISSN:
0028-0836
Pmid:
40240608


Language:
English
Keywords:
Pubs id:
2118918
Local pid:
pubs:2118918
Deposit date:
2025-05-22
ARK identifier:

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