Oesophageal atresia with no distal tracheoesophageal fistula: Management and outcomes from a population-based cohort.

Journal article

Purpose

To describe the incidence and outcomes to one-year in infants born with oesophageal atresia (OA) with no distal tracheoesophageal fistula within a population cohort.

Method

A prospective multicentre population cohort study was undertaken of all infants born with OA investigating clinical outcomes up to one year following initial surgery. Outcomes of infants with OA and a lower pouch fistula have previously been reported. A subgroup analysis describing the outcomes of infants with OA and no tracheoesophageal fistula, (Type A) and those with only an upper pouch fistula, (Type B) was performed.

Main Results

Twenty-one of 151 infants were diagnosed with Type A or B oesophageal atresia (14%). Fifteen were Type A (71%) and 6 Type B (29%). With the exception of an infant with Type A, who died before reconstruction; all but four infants (all Type B) underwent more than one operation. Median time to delayed primary anastomosis in infants with Type A and Type B was 82 days (75-89 days) (n=7). The median time to oesophageal replacement was 94 days (89-147 days) (n=8). Median length of stay for infants with Type A or B OA from first operation to first discharge was 101 days (31-123 days).

Conclusions

Oesophageal atresia with no distal tracheoesophageal fistula is uncommon. Infants with

Authors: Long, A; Tyraskis, A; Allin, B; Burge, D; Knight, M

• Publication status: Published
• Peer review status: Peer reviewed
• Publisher: Elsevier
• Journal: Journal of Pediatric Surgery
• Volume: 52
• Issue: 2
• Pages: 226-230
• Publication date: 2016-11-01
• Acceptance date: 2016-09-08
• DOI: 10.1016/j.jpedsurg.2016.11.008
• EISSN: 1531-5037
• ISSN: 0022-3468
• Language: English
• Keywords: Infant, Newborn; Prospective Studies; Anastomosis, Surgical; Long gap OA; Female; Esophagus; Cohort study; Male; Treatment Outcome; Incidence; Tracheoesophageal fistula; BAPS-CASS; Humans; Oesophageal atresia; Esophageal Atresia