Heart Rhythm UK position statement on clinical indications for implantable cardioverter defibrillators in adult patients with familial sudden cardiac death syndromes.

Journal article

Whilst the decision regarding defibrillator implantation in a patient with a familial sudden cardiac death syndrome is likely to be most significant for any particular individual, the clinical decision-making process itself is complex and requires interpretation and extrapolation of information from a number of different sources. This document provides recommendations for adult patients with the congenital Long QT syndromes, Brugada syndrome, catecholaminergic polymorphic ventricular tachycardia, hypertrophic cardiomyopathy, and arrhythmogenic right ventricular cardiomyopathy. Although these specific conditions differ in terms of clinical features and prognosis, it is possible and logical to take an approach to determining a threshold for implantable cardioveter-defibrillator implantation that is common to all of the familial sudden cardiac death syndromes based on estimates of absolute risk of sudden death.

Authors: Garratt, C; Elliott, P; Behr, E; Camm, A; Cowan, C

• Publication status: Published
• Journal: Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology
• Volume: 12
• Issue: 8
• Pages: 1156-1175
• Publication date: 2010-08-01
• DOI: 10.1093/europace/euq261
• EISSN: 1532-2092
• ISSN: 1099-5129
• Language: English
• Keywords: Arrhythmias, Cardiac; Heart Rhythm UK Familial Sudden Cardiac Death Syndromes Statement Development Group; Great Britain; Humans; Cardiomyopathies; Adult; Defibrillators, Implantable; Death, Sudden, Cardiac