Journal article
Cardiac energy metabolism is disturbed in Fabry disease and improves with enzyme replacement therapy using recombinant human galactosidase A.
- Abstract:
-
AIMS: In vitro studies have shown impairment of energy metabolism in cardiac fibroblasts from Fabry patients. A recent in vivo study reported an association between cardiac energy metabolism and increased myocardial mass in Fabry patients. We therefore assessed possible disturbances of cardiac energy metabolism in Fabry patients by in vivo (31)P-MR-spectroscopy. Additionally, the effect of enzyme replacement therapy (ERT) on cardiac energetics was tested. METHODS AND RESULTS: Twenty-three pa...
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- Publication status:
- Published
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- Publisher copy:
- 10.1093/eurjhf/hfq211
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Bibliographic Details
- Journal:
- European journal of heart failure
- Volume:
- 13
- Issue:
- 3
- Pages:
- 278-283
- Publication date:
- 2011-03-01
- DOI:
- EISSN:
-
1879-0844
- ISSN:
-
1388-9842
- Source identifiers:
-
124879
Item Description
- Language:
- English
- Keywords:
- Pubs id:
-
pubs:124879
- UUID:
-
uuid:ab8be4d7-91b5-45b0-95ae-bb5db369b1b0
- Local pid:
- pubs:124879
- Deposit date:
- 2012-12-19
Terms of use
- Copyright date:
- 2011
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