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Fibrogenesis imperfecta ossium.

Abstract:

The clinical features, investigation, treatment and outcome of two adults with fibrogenesis imperfecta ossium are described. In this rare acquired disorder of bone, normal lamellar collagen is replaced by structurally unsound collagen-deficient tissue, which leads to extreme bone fragility and ununited fractures. Transmission microscopy and SEM showed striking ultrastructural changes in bone structure and mineralisation. Both patients had monoclonal IgG paraproteins in the plasma and one excr...

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Publication status:
Published

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Institution:
University of Oxford
Department:
Oxford, MSD, NDORMS
Athanasou, N More by this author
Journal:
The Journal of bone and joint surgery. British volume
Volume:
77
Issue:
5
Pages:
820-829
Publication date:
1995-09-05
ISSN:
0301-620X
URN:
uuid:8c867da0-aac7-4618-87eb-14fd9caf4efd
Source identifiers:
103914
Local pid:
pubs:103914

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