- Four cases showing a unique combination of scarring conjunctivitis and widespread blistering, commencing in childhood are described. In all cases linear deposits IgA were present at the dermo-epidermal junction in association with low titres of circulating IgA antibasement membrane zone antibody in three cases. The relationship of this entity to chronic bullous disease of childhood, cicatricial pemphigoid and linear IgA disease of adults is as yet unclear and it may be a distinct bullous dermatosis.
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Childhood cicatricial pemphigoid with linear IgA deposits.
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