Search results - ORA - Oxford University Research Archive

1 - 5 of 5

1

Journal article

Inhibition of calcium uptake via the sarco/endoplasmic reticulum Ca2+-ATPase in a mouse model of Sandhoff disease and prevention by treatment with N-butyldeoxynojirimycin.

Pelled, D, Lloyd-Evans, E, Riebeling, C, et al.
2003-08-01

2

Journal article

Restricted ketogenic diet enhances the therapeutic action of N-butyldeoxynojirimycin towards brain GM2 accumulation in adult Sandhoff disease mice.

Denny, C, Heinecke, K, Kim, Y, et al.
2010-06-01

3

Journal article

Membrane disruption and cytotoxicity of hydrophobic N-alkylated imino sugars is independent of the inhibition of protein and lipid glycosylation.

Mellor, H, Platt, F, Dwek, R, et al.
2003-09-01

4

Journal article

Lipids on trial: the search for the offending metabolite in Niemann-Pick type C disease.

Lloyd-Evans, E, Platt, F
2010-04-01

5

Journal article

N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis.

Kasperzyk, J, El-Abbadi, M, Hauser, E, et al.
2004-05-01

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